Six Obscure Hearing Disorders

There are a lot of ways to have hearing issues. Sure, you can stand in the front of the speakers at too many concerts or just be getting old, but there are some exotic conditions too. If you want to have some good party talking points, try one of these rare syndromes on for size.

  • Ménière’s disease
    A disorder of the inner ear that not only produces vertigo, but also incessant ringing, hearing loss, and pressure “pops” in the ear. The causes are murky, with some combination of fluid buildup, infection, autoimmune issues, head trauma, and genetics at work. Because of this, treatment is usually varied and complicated.
  • Benign Paroxysmal Positional Vertigo (BPPV)
    This condition stems from an accumulation of calcium carbonate crystals in the inner ear. And yes, they’re also known as ear rocks (though the technical term is otoconia). Sometimes the condition just goes away, but a range of drugs, surgery, and even head exercises meant to get the ear rocks to roll out of the inner ear are often prescribed.
  • Labyrinthitis
    As a result of infection affecting nerve transmitters and the inner ear, swelling disrupts communication to the brain (vision can also be interrupted). If treated quickly with antiviral or antibacterial drugs it’s treatable, but long-term damage can occur if it is not treated. Dizziness and nausea are also symptoms.
  • Acoustic neuroma
    A rare condition caused by the development of a benign tumor that interrupts hearing and balance information from being transmitted to the brain. Surgery is the common treatment to prevent further complications.
  • Autoimmune inner ear disease (AIED)
    Not well understood, AIED results in the immune system attacking the inner ear, leading to hearing loss, tinnitus, and balance issues. Steroids and blood filtration (plasmapheresis) are common treatments, along with hearing aids.
  • Otosclerosis
    This hardening of the inner ear’s bones is usually a hereditary condition. There are a variety of treatments to deal with what will inevitably lead to continual degradation of hearing.